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Pathoanatomical features of Shar-Pei's hereditary amyloidosis

Kulikov E.V., Vatnikov Y.A., Parshina V.I., Popova I.A. and Sahno N.V.
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Kulikov E.V.: Peoples' Friendship University of Russia
Vatnikov Y.A.: Peoples' Friendship University of Russia
Parshina V.I.: Peoples' Friendship University of Russia
Popova I.A.: Peoples' Friendship University of Russia
Sahno N.V.: Orel State Agrarian University

Russian Journal of Agricultural and Socio-Economic Sciences, 2016, vol. 58, issue 10, 183-189

Abstract: Shar-Pei's amyloidosis is a hereditary disease which is characterized by amyloid deposition in stromal-vascular organs. The contributory cause of amyloidosis is а genetic disease Shar Pei's fever. Amyloidosis is based on enzymatic processes abnormality in connective-tissue cells. Enzymopathy is followed by synthesis of the abnormal fibrous protein entering strong compound with proteins of plasma and glycosaminoglycans of ground substance of connective tissue.

Keywords: AMYLOID; SHAR-PEI'S FEVER; HEREDITARY DISEASE; AMYLOIDOBLASTS; AMYLOIDOCLASTS (search for similar items in EconPapers)
Date: 2016
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